Spontaneous Anterior Lens Capsule Rupture Of a Patient with Alport Syndrome - A Case Report

Kalina Trifonova; George Jordanoff; Valentin Stoyanov; Kiril Slaveykov

doi:10.3889/oamjms.2017.196

Authors

Kalina Trifonova Trakijski Universitet Stara Zagora, Meditsinski fakultet, Otorhinolaryngology, Stara Zagora
George Jordanoff Trakijski Universitet Stara Zagora, Meditsinski fakultet, Otorhinolaryngology, Stara Zagora
Valentin Stoyanov Trakijski Universitet Stara Zagora, Meditsinski fakultet, Otorhinolaryngology, Stara Zagora
Kiril Slaveykov Trakijski Universitet Stara Zagora, Meditsinski fakultet, General Medicine, Armeiska 11, Stara Zagora 6000

DOI:

https://doi.org/10.3889/oamjms.2017.196

Keywords:

Alport syndrome, Genetic disease, Lens, Capsule rupture, Phacoaspiration

Abstract

BACKGROUND: Alport syndrome is a progressive genetic disease which is characterised by glomerulonephritis, sensorineural deafness and ocular abnormalities.We aimed to present a clinical case of a patient with Alport syndrome with spontaneous anterior lens capsule rupture.

CASE REPORT: A 16-year-old male with histologically proven Alport syndrome was hospitalised in the Department of Ophthalmology, University Hospital â€žProf. Stoyan Kirkovichâ€œ, Stara Zagora with low vision, pain, redness, high IOP and rupture of the anterior lenticular capsule of the right eye. Phacoaspiration was successfully performed (Millenium, Bausch& Lomb, Rochester, New York, USA) with the bimanual irrigation-aspiration system (Geuder AG, Heidelberg, Germany) with excellent visual results.

CONCLUSION: As the syndrome is quite rare and can lead to diagnostic difficulties for the ophthalmologist complications such as spontaneous or traumatic rupture of the capsule are not uncommon. In such cases, phacoaspiration is an efficient method for clear lens extraction after ruptures of the anterior lenticular capsule of young patients with Alport syndrome.

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