A Very Rare Case of Cor Triatriatum with Severe Mitral Regurgitation

Selman Dumani; Ermal Likaj; Edlira Ruci; Ervin Bejko; Ali Refatllari

doi:10.3889/oamjms.2018.176

Authors

Selman Dumani University Hospital Center "Mother Tereza", Tirana http://orcid.org/0000-0002-7971-0210
Ermal Likaj University Hospital Center "Mother Tereza", Tirana
Edlira Ruci University Hospital Center "Mother Tereza", Tirana
Ervin Bejko University Hospital Center "Mother Tereza", Tirana
Ali Refatllari University Hospital Center "Mother Tereza", Tirana

DOI:

https://doi.org/10.3889/oamjms.2018.176

Keywords:

Cor triatriatum, Congenital heart disease, Mitral regurgitation

Abstract

BACKGROUND: Cor triatriatum sinister is rare congenital heart disease. It is mainly presented in childhood and often accompanied with other congenital anomalies. The cases with cor triatriatum treated surgically in adults and accompanied with severe mitral regurgitation are very rare.

CASE REPORT: We present a case with diagnosed cor triatriatum and severe mitral regurgitation. The diagnose was made by echocardiography. She was a female 25 years that was hospitalised with signs of heart failure NYHA II-III.

CONCLUSION: We performed the resection of the membrane in the left atrium and repair of a mitral valve according to Alfieri. The patient did very well after the surgery.

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