BehÃ§et's Disease â€“ Case Presentation and Review Literature
Keywords:Aft syndrome, BehÃ§et's syndrome, Mucosal ulceration, HLA-B51
BACKGROUND: BehÃ§et's syndrome is associated with inflammation of various areas of the body. Sy. Behcet is a rare, chronic, recurrent disease characterised by changes in the: Arteries that supply blood to the body's tissues, veins that take the blood back to the lungs, the back of the eye's retina, brain, joints, skin and bowels. There is a close correlation between the geographical distribution of HLA-B51 and its prevalence. In the etiopathogenesis, there are indications of genetic susceptibility associated with environmental influence. Although aetiology is not yet known, it is thought of viral or autoimmune genes but is not yet confirmed by relevant analysis.
CASE REPORT: This was a case of a 29 years old young female presenting with recurrent oral and genital ulcers. Eye lesions usually start in one eye and then pass to the other eye. They are like iridocyclitis extending very quickly to another eye. Three months later, a few shifts were introduced in the form of small initial ulcers, which for 4-5 days have been enlarged and then epithelized by leaving the catapult in the genital mucus. In the skin of the lower extremities, papules appear to be as large as corn grain.
CONCLUSION: Diagnosis of BehÃ§et's syndrome is determined based on eye changes, oral mucous and genital mucosa. Treatment of BehÃ§et's syndrome depends on the severity and the location of its manifestations.
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