Congenital Cystic Adenomatoid Malformations Type 1: Case Report

Andi Dwi Bahagia Febriani; Nurul Sylvana Shoraya; Ema Alasiry

doi:10.3889/oamjms.2022.8539

Authors

Andi Dwi Bahagia Febriani Department of Pediatrics, Faculty of Medicine, Hasanuddin University, Makassar, Indonesia; Dr. Wahidin Sudirohusodo General Hospital, Makassar, Indonesia https://orcid.org/0000-0001-6076-9995
Nurul Sylvana Shoraya Departement of Pediatrics, Faculty of Medicine, Hasanuddin University, Makassar, Indonesia
Ema Alasiry Department of Pediatrics, Faculty of Medicine, Hasanuddin University, Makassar, Indonesia; Dr. Wahidin Sudirohusodo General Hospital, Makassar, Indonesia

DOI:

https://doi.org/10.3889/oamjms.2022.8539

Keywords:

Congenital cystic adenomatoid malformations, Respiratory distress, Lung malformation

Abstract

BACKGROUND: Congenital cystic adenomatoid malformation (CCAM) is a group of multicystic and non-cystic masses due to abnormal lung development. The incidence ranges from 1: 10,000 to 1: 35,000 pregnancies.

CASE REPORT: We report a case of a 3-day male baby presented with worsening respiratory distress, X-ray and chest CT were suggestive of CCAM, and sepsis.

CONCLUSION: The current case adds to the collective clinical and radiological knowledge of this rare congenital lung disorder.

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