Herlyn Werner Wunderlich Syndrome with Hematocolpos Symptom

Muhammad Rusda; Amru Umara; Andrina Yunita Murni Rambe

doi:10.3889/oamjms.2019.406

Authors

Muhammad Rusda Division of Reproductive Endocrinology and Infertility, Department of Obstetrics and Gynaecology, Medical Faculty, Universitas Sumatera Utara, RSUP Haji Adam Malik Jl. Dr T. Mansur No.5, Medan 20154, Indonesia
Amru Umara Division of Reproductive Endocrinology and Infertility, Department of Obstetrics and Gynaecology, Medical Faculty, Universitas Sumatera Utara, RSUP Haji Adam Malik Jl. Dr T. Mansur No.5, Medan 20154, Indonesia
Andrina Yunita Murni Rambe Division of Reproductive Endocrinology and Infertility, Department of Obstetrics and Gynaecology, Medical Faculty, Universitas Sumatera Utara, RSUP Haji Adam Malik Jl. Dr T. Mansur No.5, Medan 20154, Indonesia

DOI:

https://doi.org/10.3889/oamjms.2019.406

Keywords:

Herlyn werner wunderlich syndrome, laparoscopy, vaginal septal resection, hematocolpos

Abstract

BACKGROUND: Uterodidelphys with obstructed hemivagina and ipsilateral renal agenesis is referred to as the Herlyn Werner Wunderlich (HWW) syndrome. Herlyn-Werner-Wunderlich (HWW) syndrome is a very rare congenital anomaly of the urogenital tract involving MÃ¼llerian ducts and Wolffian structures, and it is Werner by the triad of uterus didelphys, obstructed hemivagina and ipsilateral renal agenesis.

CASE REPORT: Here, we describe a 17-year-old female patient presented with severe and increasing cyclical abdominal pain. She attained menarche 3 years back. The patient had irregular and scanty menstruation associated with dysmenorrhoea. On physical examination, secondary sexual characters were well developed, and on palpation, lower abdomen tenderness was not present. Diagnosed with HWW syndrome, who was taken up for diagnostic sonography and MRI, followed by vaginal septal resection,

CONCLUSION: In addition to a definitive diagnosis, this approach helped in symptomatic relief to the patient.